John Libbey Eurotext

Adult-onset Rasmussen encephalitis associated with focal cortical dysplasia Volume 19, issue 4, December 2017


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1 Department of Neurology,
2 Department of Anatomopathology,
3 Department of Nuclear Medecine, Cliniques universitaires Saint-Luc, Université Catholique de Louvain, Bruxelles
4 Department of Neurology, Centre Hospitalier Neurologique William Lennox, Ottignies, Belgium
* Correspondence: Katharina Hohenbichler Department of Neurology, Klinikum Harlaching, Sanatoriumsplatz 2, 81545 Munich, Germany

Rasmussen encephalitis is a rare, devastating condition, typically presenting in childhood. Cases of adult-onset Rasmussen have also been described, but the clinical picture is less defined, rendering final diagnosis difficult. We present a case of adult-onset Rasmussen encephalitis with dual pathology, associated with focal cortical dysplasia and encephalitis. We interpreted the Rasmussen encephalitis to be caused by severe and continuous epileptic activity due to focal cortical dysplasia. The best therapeutic approach for such cases remains unclear.