Figure 2.
Capillary naevus and ocular vascular malformation in patients with phacomatosis pigmentovascularis. Facial naevus flammeus is darker in a patient with glaucoma (A) than a patient without glaucoma (B). C, D) Dilated episcleral vessels with increased density present a reticulate appearance with episcleral melanosis. E, F) Dark and total perilimbal episcleral hyperpigmentation are shown in the eyes. G) Fundus fluorescein angiography shows peripheral retinal vascular leakage, venous shunts and tortuous capillaries. H) Choroidal haemangioma (white arrow) demonstrated by B-scan ultrasonography.