John Libbey Eurotext

European Journal of Dermatology


Treatments and outcomes in juvenile linear scleroderma: a narrative systematic review Volume 28, issue 5, September-October 2018


1 Department of Dermatology and Pediatric Dermatology, Necker-Enfants Malades Hospital, Assistance Publique Hôpitaux de Paris (APHP), 75015 Paris, France
2 Centre Hospitalier Régional Universitaire (CHRU) Tours, Department of Dermatology, 37044 Tours Cedex 9, France
3 Universities of Nantes and Tours, SPHERE-INSERM 1246, 37000 Tours, France
a These authors contributed equally

Localized scleroderma (morphea) is a rare chronic inflammatory disease that affects skin and/or underlying subcutaneous tissues and can lead to permanent functional or cosmetic disabilities [1]. Linear scleroderma (LS) is the most frequent presentation in children [2, 3]. LS most frequently affects the limbs or the face, with two possible subgroups: the head/face “en coup de sabre” (ECS) form and progressive hemi-facial atrophy or Parry-Romberg syndrome (PRS) [1]. The long-term outcome of LS is not [...]