John Libbey Eurotext

Annales de Biologie Clinique


Hémophagocytose lymphohistiocytaire familiale : une entité conduisant à un décès précoce Volume 79, numéro 5, Septembre-Octobre 2021


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1 Biology Laboratory, Monastir Maternity and Neonatology Center, Tunisia
2 Department of Neonatology, Monastir Maternity and Neonatology Center, Tunisia
* Correspondance

A one-day-old newborn was admitted for immediate presentation of a tumor syndrome with extensive purpuric lesions. Clinical examination revealed hepatosplenomegaly and recurrent fever. This neonate was born from a pregnancy carried to term without antenatal anomalies and then delivered by emergency cesarean section for acute fetal distress. Exploration of the family history revealed the notion of a 3rd degree consanguineous marriage, 2 deaths in the fraternity in a context of disseminated intravascular [...]