John Libbey Eurotext

European Journal of Dermatology


Phacomatosis pigmentovascularis type II Volume 8, numéro 8, December 1998

Clinique Dermatologique CHRU, F-59037 Lille Cedex, France.
  • Page(s) : 569-72
  • Année de parution : 1999

Phacomatosis pigmentovascularis (PPV) is a rare condition first described by Ota in 1947 [1]. This entity is characterized by the simultaneous occurrence of a pigmented and a vascular nevus. Classification is based on the type of pigmented nevus. Each type is subdivided into two subtypes: (a) when only cutaneous involvement is present, (b) when cutaneous and systemic disease are found. Two cases of PPV type II are reported herein. One [...]