John Libbey Eurotext

European Journal of Dermatology

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A case of lymphoma-associated haemophagocytic syndrome in advanced-stage mycosis fungoides Volume 30, numéro 5, September-October 2020

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Auteurs
1 Department of Dermatology, Faculty of Medicine, Institute of Medical, Pharmaceutical and Health Sciences, Kanazawa University, Kanazawa, Japan
2 Department of Dermatology, Noto General Hospital, Nanao, Japan

Haemophagocytic syndrome (HPS) is a systemic life-threatening disease characterized by fever, hepatosplenomegaly, and pancytopenia. HPS generally develops in immunocompromised patients or in association with autoimmune diseases [1]. Lymphoma-associated haemophagocytic syndrome (LAHS) can develop in anaplastic T-cell lymphoma and subcutaneous panniculitis-like T-cell lymphoma, but it is a very rare clinicopathological entity in patients with mycosis fungoides (MF) [2].A 72-year-old woman was diagnosed [...]