Department of Dermatology, Hamamatsu University School of Medicine,
1-20-1 Handa-yama, Hamamatsu 431-3192, Japan.
macularis eruptiva perstans (TMEP) is a rare form
of cutaneous mastocytosis, characterized by multiple brownish-red confluent
macules and telangiectasia . Most patients with this disease have only
skin lesions with a good prognosis. However, some cases exhibit systemic
involvement, such as hematologic disorders. There have been 5 cases of mastocytosis
with polycythemia rubra reported in the literature [2-6]. Four of 5 patients