John Libbey Eurotext

European Journal of Dermatology


Purpura-associated congenital lymphedema Volume 19, numéro 6, November-December 2009

Department of Pediatric Medicine, Anna Meyer Children’s Hospital, Viale Pieraccini, 24, 50132 Florence, Italy, Department of Cardiology, University of Florence, Florence, Italy, Department of Dermatology, University of Florence, Florence, Italy, Department of Human Oncology and Pathology, University of Florence, Florence, Italy

An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.