European Journal of Dermatology
MENUExtranodal natural killer/T-cell lymphoma, nasal type: a Spanish multicentric retrospective survey Volume 28, numéro 1, January-February 2018
Auteurs
4 Dermatology Department,
Hospital Universitari de Bellvitge,
ĹHospitalet de Llobregat,
Barcelona, Spain
Hospital Universitari de Bellvitge,
ĹHospitalet de Llobregat,
Barcelona, Spain
6 Dermatology Department,
Hospital Universitario de Gran Canaria Doctor Negrín,
Las Palmas de Gran Canaria,
Islas Canarias, Spain
Hospital Universitario de Gran Canaria Doctor Negrín,
Las Palmas de Gran Canaria,
Islas Canarias, Spain
11 Dermatology Department,
Hospital de Sant Joan Despí-Moisès Broggi,
Sant Joan Despí,
Barcelona, Spain
Hospital de Sant Joan Despí-Moisès Broggi,
Sant Joan Despí,
Barcelona, Spain
* Reprints
- Mots-clés : extranodal natural killer/T-cell lymphoma nasal type, ENKTL, Spain, histology, clinical, treatment, prognosis, survival
- DOI : 10.1684/ejd.2017.3205
- Page(s) : 64-70
- Année de parution : 2018
Extranodal natural killer/T-cell lymphoma, nasal type (ENKTL), is an aggressive subtype of peripheral lymphoma characterized by heterogeneous clinical features, an angiocentric growth pattern, prominent necrosis, a cytotoxic phenotype, and association with Epstein-Barr virus (EBV) [1, 2]. Its incidence is higher in regions such as Asia, Mexico, and Central and South America than in western countries [3]. In more than 80% of reported cases, the disease presents in the nasal cavity, whereas in the [...]