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Jerking during absences: video-EEG and polygraphy of epileptic myoclonus associated with two paediatric epilepsy syndromes Volume 23, numéro 1, February 2021

TEST YOURSELF

(1) What are the main epilepsy syndromes in childhood that may include, among seizures types, the negative cortical myoclonus?

 

(2) In clinical practice, what is the technical set up used to enhance negative myoclonus during EEG recording?

 

(3)What is the EEG correlate of cortical negative myoclonus?

 

 

 

 

 

 

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Answers

(1) Atypical benign focal epilepsy in childhood, encephalopathy related to status epilepticus during slow sleep (ESES) and progressive myoclonic epilepsies.

 

(2) Electromyogram (EMG) on agonist and antagonist muscles involved in the observed clinical phenomenon, recorded with 2 cup electrodes placed 2 cm apart. Ask the patient to stay up or seat (not lay down) and outstretch arms to make the muscular tone. The atonic phase will be visible on EMG polygraphy as interruption of the muscular tone.

 

 

(3) In pure epileptic negative myoclonus, the EMG silent period is preceded by a cortical spike (thus named cortical negative myoclonus).

 

 

 

 

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