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Epileptic Disorders

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Epileptic spasms in epilepsy with myoclonic-atonic seizures (Doose syndrome) Volume 18, numéro 3, September 2016

Figure 1

Patient 1. Background activity of 5 Hz. Intermittent theta high-amplitude activity in frontal regions.

Figure 2

Patient 1. A burst, lasting approximately eight seconds, of repetitive diffuse high-amplitude spike/polyspikes-and-slow-wave complexes with a frequency of approximately 1 Hz.

Figure 3

Patient 1. From drowsiness, electroclinical ES characterized by sudden flexion and contraction of proximal limb muscles and head, lasting around one second. Clinical symptoms were preceded by a burst of diffuse polyspikes, followed by a high-voltage slow wave lasting 700 ms, and by a diffuse flattening lasting 2 seconds.

Figure 4

Patient 2. Cluster of spasms.

Figure 5

Patient 3. EEG recording with EMG (electrodes on the right deltoid). The EEG correlate to each of these events was a short phase of low-voltage fast activity preceding a higher-voltage bilateral slow wave, without clear attenuation between episodes. On EMG, the seizures were correlated with a diamond-shaped pattern, consistent with spasms.