Figure 1
Ictal EEG of Case 1 (A, B) and Case 3 (C). All patients developed myoclonic seizures between one week and three months of age. Myoclonic seizures () occurred spontaneously, and also appeared in response to sudden unexpected acoustic or tactile stimuli (↑). Representative ictal EEGs are shown. In Case 1, ictal EEG reveals a diffuse irregular spike-and-wave complex corresponding to spontaneous myoclonic jerks (A) and high-voltage diffuse slow waves corresponding to stimulation-induced myoclonic jerks (B). The ictal EEG of Case 3 shows spike-and-wave complexes corresponding to spontaneous myoclonic jerks (C).