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Absence status epilepticus in monozygotic twins with Jeavons syndrome Volume 10, numéro 3, September 2008

Figure 1 The patient (twin 2) was in a conscious, alert, resting state. The clinical manifestation was paroxysmal, fast, repetitive jerks of the eyelids. Video-EEG showed main α background activity, bilateral frequent high amplitude 2.5-6HZ GSWD and sharp and slow wave complexes, which occurred immediately within 0.5-2s after eye closure (arrow) and briefly.

Figure 2 Status epilepticus of EMA (twin 1). The clinical manifestation was continuous, fast, arrhythmic jerks of the eyelids, often associated with retropulsion and repetitive brief lapses of consciousness. The patients could not identify their parents, distinguish right from left or perform simple calculations, and there was slowness of judgment and planned movements. This lasted for four hours, 50 minutes and two hours, 45 minutes in twin 1 and twin 2, respectively. The video-EEG demonstrated continuous, generalized, high to very high amplitude, irregular polyspike and spike-wave discharges and blinking artifacts (arrow), shown before trains of spike-wave discharges.