John Libbey Eurotext

European Journal of Dermatology

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Telangiectasia macularis eruptiva perstans: a neglected type of mastocytosis with exclusively cutaneous involvement? A case series Volume 29, numéro 2, March-April 2019

Illustrations

  • Figure 1
  • Figure 2

Tableaux

Auteurs
1 Institute of Dermatology Department of Clinical-Surgical, Diagnostic and Paediatric Sciences, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy
2 Department of Hematology Oncology, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy
3 Unit of Anatomic Pathology, Department of Molecular Medicine, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy
4 Department of Pediatrics, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy
* Reprints
  • Mots-clés : cutaneous mastocytosis, systemic mastocytosis, telangiectasia macularis eruptiva perstans, maculopapular cutaneous mastocytosis
  • DOI : 10.1684/ejd.2019.3532
  • Page(s) : 174-8
  • Année de parution : 2019

Background

Telangiectasia macularis eruptiva perstans (TMEP) is a rare form of cutaneous mastocytosis (CM). Although TMEP has been traditionally thought to be restricted to the skin, a recent retrospective multicentric study established a diagnosis with systemic involvement of mastocytosis in 47% patients affected by TMEP and aggressive systemic mastocytosis in 9%.