Sang Thrombose Vaisseaux
MENUAfibrinogenemia: a rare disease requiring a multidisciplinary care Volume 34, issue 4, July-August 2022
Authors
1 CREATIF, Hôpital Lariboisière, service de cardiologie, 2, rue Ambroise Paré, 75010 Paris, France
2 Hôpital Saint Joseph, service de médecine vasculaire, 185, rue Raymond Losserand, 75014 Paris, France
3 Clinique de l’Alma, centre de pathologie vasculaire, 166, rue de l’Université, 75007 Paris, France
4 Hôpital Saint-Louis, service d’hématologie, 1, avenue Claude Vellefaux, 75010 Paris, France
- Key words: afibrinogenemia, hemorrhagic disease, bleeding, fibrinogen
- DOI : 10.1684/stv.2022.1214
- Page(s) : 173-5
- Published in: 2022
Afibrinogenemias are exceptional hereditary pathologies whose hemorrhagic risk is major. Their management and complications can be complex because fibrinogen, apart from its role in coagulation, has a role in hemostasis and thrombosis and has many pleiotropic functions in healing, inflammation, etc.