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Afibrinogenemia: a rare disease requiring a multidisciplinary care Volume 34, issue 4, July-August 2022

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Authors
1 CREATIF, Hôpital Lariboisière, service de cardiologie, 2, rue Ambroise Paré, 75010 Paris, France
2 Hôpital Saint Joseph, service de médecine vasculaire, 185, rue Raymond Losserand, 75014 Paris, France
3 Clinique de l’Alma, centre de pathologie vasculaire, 166, rue de l’Université, 75007 Paris, France
4 Hôpital Saint-Louis, service d’hématologie, 1, avenue Claude Vellefaux, 75010 Paris, France

Afibrinogenemias are exceptional hereditary pathologies whose hemorrhagic risk is major. Their management and complications can be complex because fibrinogen, apart from its role in coagulation, has a role in hemostasis and thrombosis and has many pleiotropic functions in healing, inflammation, etc.