Epileptic Disorders
MENUElectrical status epilepticus “invisible” to surface EEG in late-onset Rasmussen encephalitis Volume 10, numéro 3, September 2008
Illustrations
Jinane Fattouch, Carlo Di Bonaventura, Giancarlo Di Gennaro, Pier Paolo Quarato, Simona Petrucci, Mario Manfredi, Massimilano Prencipe, Vincenzo Esposito, Anna Teresa Giallonardo
Department of Neurological Sciences, Neuromed Institute of Pozzilli (IS), University of Rome “La Sapienza”, Italy
- Mots-clés : late-onset Rasmussen encephalitis, status epilepticus, subdural electrodes
- DOI : 10.1684/epd.2008.0200
- Page(s) : 219-22
- Année de parution : 2008
Rasmussen’s encephalitis (RE) is a chronic, progressive disease that typically occurs in childhood, rarely in adulthood. When it does occur in adulthood, it may be associated with atypical electro-clinical features, and neuroimaging alterations usually help diagnosis. Unlike childhood forms, in which epilepsia partialis continua is usually observed, the EEG pattern in adult variants may be aspecific. We describe a highly interesting case of late-onset RE in which an electrical status epilepticus was not detected by the surface EEG, but by a recording with subdural electrodes.