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Epileptic Disorders

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Ictus emeticus presenting as an unusual seizure type in chromosome 22q11.2 deletion syndrome Volume 19, numéro 1, March 2017

Figure 1

The EEG background showed asymmetric and discontinued delta rhythm across the left posterior temporal lobe during left leg flexion and retching (A). Ictal EEG documented symmetric and synchronized delta rhythm over posterior temporal regions during vigorous vomiting (B).

Figure 2

Axial T1 3D FSPGR demonstrated right hemisphere polymicrogyria (PMG) with a flattened cortical surface and excessive surface convolutions (A: upper panels; white arrows). T2-weighted images revealed heterotopic neurons in the right frontal white matter zone (A: lower panels; white arrows). Interictal FDG-PET exhibited diffuse hypometabolism, especially in the right parietal region (B). Emetic frequency significantly decreased after phenobarbital administration in April 2014 (C: blank bars), and symptom-free intervals were prolonged in conjunction with ketogenic diet therapy (D: black bars). When the patient discontinued ketogenic diet therapy between November and December 2015, the symptom-free interval was significantly shortened (D: black arrows). *P<0.05.