John Libbey Eurotext

European Journal of Dermatology


Phacomatosis pigmentovasculosebacea: an unusual case of phacomatosis multiplex Volume 13, numéro 3, May 2003

Department of Dermatology, College of Medicine, National Cheng Kung University, 138 Sheng-Li Road, 704 Tainan, Taiwan. Rudolf Happle: Department of Dermatology, University of Marburg, Deutschhausstr. 9, 35033 Marburg, Germany
  • Mots-clés : nevus, phacomatosis, twin spot phenomenon
  • Page(s) : 231-3
  • Année de parution : 2003

A 13-year-old Taiwanese boy had an unusual combination of nevus fuscocoeruleus, large café-au-lait macules, nevus achromicus, large telangiectatic nevi and systematized nevus sebaceus. The term "phacomatosis pigmentovasculosebacea" is proposed to describe the concurrence of these multiple nevi derived from pigmentary, vascular and epithelial cells.