John Libbey Eurotext

European Journal of Dermatology


Bullous pemphigoid accompanied by IgA nephropathy and atypical haemolytic uraemic syndrome Volume 28, numéro 3, May-June 2018


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1 Department of Dermatology,
2 Department of Hematology,
3 Department of Nephrology, Faculty of Medicine, University of Tsukuba, 1-1-1 Tennodai, Tsukuba, Ibaraki 305-8575, Japan

Bullous pemphigoid (BP) is an autoimmune skin-blistering disease caused by IgG autoantibodies against BP180 and/or BP230. Although BP has been reported to be associated with several diseases, coexistence of BP and autoimmune renal disease is rare. Here, we describe a BP patient who had been affected by IgA nephropathy which led to atypical haemolytic uremic syndrome (aHUS).A 38-year-old female with a two-year history of IgA nephropathy presented with itchy erythema and blisters on her trunk and extremities. [...]