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 Printable version |
Treatment of mucinous appendiceal neoplasm |
Hépato-Gastro. Volume 18, Number 6, 581-8, Novembre-Décembre 2011, Mini-revue
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 Résumé
Texte intégral
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Author(s) : Diane Goéré, Peggy Dartigues, Dominique Elias |
Summary : Appendiceal tumors are rare entities, usually incidentally diagnosed. Histological analysis of the appendices indicates the presence of a mucocele in 0.07 to 0.3% of cases. Appendiceal mucocele is a term used for the gross and macroscopic description of a dilated appendix, it may be related to simple retention cyst, to mucinous cystic neoplasm, or to mucinous adenocarcinoma. Rupture into the peritoneal cavity of all appendiceal mucoceles, except for a simple retention cyst, results in release of mucus and epithelial cells in the peritoneal cavity resulting in a peritoneal pseudomyxoma. This emphasizes that any distended appendix, whose appearance suggests a mucocele, must be handled with extreme care to avoid extravasation of mucus or rupture of mucocele in the peritoneal cavity. Treatment is primarily surgical, the extent of removal depending on the histological diagnosis. Peritoneal pseudomyxoma belongs to the rare tumors of the peritoneum for which the National Institute of Cancer (INCA) has recently organized health care delivery, including through the establishment of a network of national and regional experts (RENAPE) which patients can be addressed. |
Keywords : appendiceal mucocele, mucinous appenciceal neoplasm, pseudomyxoma, hyperthermic intraperitoneal chemotherapy |
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