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Epileptic Disorders

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Reflex seizures in Rett syndrome Volume 13, issue 4, December 2011



Figure 1 Interictal EEG of Patient 1 showing discharges over the midline (Cz), central, and frontal electrodes.



Figure 2 Ictal EEG of Patient 1. Polygraphic electrodes placed at para-vertebral cervical muscles showing the disappearance of the previous interictal epileptiform abnormalities immediately at the beginning of food intake. Ictal EEG shows a generalised high-voltage slow wave component, which was sometimes preceded by epileptiform abnormalities. Cephalic and axial loss of tone was associated with a peak of this slow component, followed by an event with rhythmic sharp waves of low or medium amplitude. Polygraph recording revealed sudden interruption of the electromyographic (EMG) potentials; this EMG silencing was more evident when the seizures were more prolonged (400 msec). A total of 12 seizures were registered; generalised high-voltage slow-wave activity was observed on the EEG following each seizure.