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Isolated flushes without permanent, fixed or other skin lesions in patients with systemic mastocytosis: a case series of 9 patients Volume 25, issue 2, April 2015

Figures


  • Figure 1
Authors
1 Centre de Référence des Mastocytoses,
AP-HP Necker-Enfants Malades,
156 Rue de Vaugirard,
75743 Paris,
France
2 Laboratoire d’hématologie Biologique AP-HP Necker-Enfants Malades,
Paris,
France
3 CNRS UMR 8147,
Hôpital Necker-Enfants malades,
Paris,
France
4 Service d’Hématologie,
CHU Caen,
France
5 Inserm,
U1068,
Marseille,
13009,
France
6 Service de Dermatologie,
Hôpital Tenon,
Paris,
France
7 Service de médecine interne,
Hôpital Nord,
Saint-Etienne,
France
8 Service de médecine interne,
CHU Lyon-Sud,
Lyon,
France
9 Unité de médecine interne,
Hôpital européen,
Marseille,
France
10 Clinique universitaire de médecine interne,
CHU Grenoble,
France
11 Service de Médecine interne,
CHU Nantes,
France
12 Service des maladies infectieuses et tropicales,
AP-HP,
Hôpital Necker-Enfants malades,
Paris,
France
13 Service d’Hématologie Adultes,
AP-HP Necker-Enfants Malades,
Paris,
France
14 Institut Imagine,
Université Paris Descartes,
Paris,
France
15 Service de Médecine interne,
Hôpital Tenon,
Paris,
France
a These authors co-directed the study.

Mastocytosis is a heterogeneous group of disorders characterized by abnormal growth and accumulation of mast cells (MCs) in one or more organ systems [1, 2]. Clinical manifestations of mastocytosis are related to the release of MC mediators or to pathological MC infiltration [1, 2]. Urticaria pigmentosa is present in almost 60% of cases of systemic mastocytosis [2-5].Flushing is a sensation of warmth accompanied by transient erythema, usually over the face, neck, ears, chest and limbs and is due [...]