European Journal of Dermatology
MENUExtramammary Paget's disease occurring in the context of Cowden syndrome: true association or mere coincidence? Volume 25, issue 1, January-February 2015
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1 Department of Dermatology,
2 Department of Pathology,
Graduate School of Medicine,
University of Toyama,
2630 Sugitani,
Toyama 930-0194,
Japan
Graduate School of Medicine,
University of Toyama,
2630 Sugitani,
Toyama 930-0194,
Japan
- DOI : 10.1684/ejd.2014.2475
- Page(s) : 89-91
- Published in: 2015
Cowden syndrome (CS) is a rare inherited disorder characterized by multiple hamartomas and an increased risk of carcinomas, such as thyroid and breast cancers [1]. Characteristic mucocutaneous manifestations include multiple facial trichilemmomas, oral mucosal papillomatoses and acral keratosis. A mutation in the phosphatase and tensin homolog (PTEN) gene has been identified as the cause of CS [2]. The present report describes a case of extramammary Paget's disease (EMPD) which developed in a Japanese [...]