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Extra medullary hematopoiesis associated to congenital dyserythropoietic anemia II in adult |
Annales de Biologie Clinique. Volume 70, Number 2, 217-20, Mars-Avril 2012, Biologie au quotidien
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 Résumé
Texte intégral
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Author(s) : Inès Jedidi, Moez Medhaffar, Manel Ghorbel, Sondes Hdiji, Faiza Makni, Moez Elloumi, Choumous Kallel |
Summary : The congenital dyserythropoietic anemias comprise a group of rare hereditary disorders of erythropoiesis characterized by anemia with ineffective erythropoiesis and morphological abnormalities of erythroblasts in the bone marrow. Congenital dyserythropoietic anemia type II or HEMPAS is the more frequent type. It is rare in adults. Extra medullary hematopoiesis is also a rare entity\; it is a physiological response to chronic anemia observed in certain hemopathies like congenital dyserythropoietic anemia type II. We report the observation of a patient for who diagnosis of extra medullary hematopoiesis associated to congenital dyserythropoietic type II was made in adulthood. |
Keywords : congenital dyserythropoietic anemia type II (CDA II), HEMPAS, extra medullary hematopoiesis |
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