John Libbey Eurotext




Purpura-associated congenital lymphedema
European Journal of Dermatology. Volume 19, Number 6, 623-5, November-December 2009, Clinical report
Free Article
Author(s) : Samantha Berti, Alessandro Pieri, Torello Lotti, Alberto Duranti, John Panelos, Maurizio De Martino, Silvia Moretti
Summary : An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.
Keywords : hereditary lymphedema type I, Milroy disease, purpura, saphenous vein insufficiency, ulceration

Purpura-associated congenital lymphedema