John Libbey Eurotext




Cutaneous polyarteritis nodosa in adult onset Still’s disease
European Journal of Dermatology. Volume 19, Number 6, 621-2, November-December 2009, Clinical report
Free Article
Author(s) : Eleni Mylona, Chariklia Vadala, Vasilios Papadakos, Dionysios Loverdos, Michael Samarkos, Athanasios Skoutelis
Summary : Adult onset Still’s disease (AOSD) is a well recognized clinical disorder characterized by a typical rash. However, there have been several atypical cutaneous findings reported in patients with AOSD. Cutaneous polyarteritis nodosa (PAN) is a necrotizing vasculitis of the small and medium sized arteries, distinguishing itself from systemic PAN by its restriction to the skin and to the neurological and osteo-muscular systems. We report the case of a patient with AOSD who is unique in having developed cutaneous polyarteritis nodosa (PAN) during the active phase of her disease. To the best of our knowledge, no previous cases of AOSD associated with a cutaneous variant of PAN have been reported.
Keywords : adult onset Still’s disease, cutaneous polyarteritis nodosa, vasculitis, pneumonitis, leflunomide

Cutaneous polyarteritis nodosa in adult onset Still’s disease