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Dyskeratosis congenita associated with Hodgkin’s disease


European Journal of Dermatology. Volume 8, Number 6, 385-7, September 1998, Gènes et peau

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Author(s) : Can BAYKAL, Nesimi BÜYÜKBABANI, Ayse KAVAK

Summary : Dyskeratosis congenita is a rare, hereditary, multisystem disorder characterized by mucocutaneous changes, pancytopenia and increased incidence of malignancy. Different types of neoplasia have been reported in association with dyskeratosis congenita. We present a second case associated with Hodgkin’s disease. Delayed appearance of dermatological signs and association with chronic hepatitis B are other unusual features of this case.

Keywords : dyskeratosis congenita, Hodgkin’s disease, leucokeratosis.)

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